Portal Cavernoma in Children: Rare Pathology with Complex Management about 3 Cases
S. Aithmadouch
*
Service de Pédiatrie Hôpital d`instruction Militaire, Rabat, Morocco.
A. Radi
Service de Pédiatrie Hôpital d`instruction Militaire, Rabat, Morocco.
K. Larbiouassou
Service de Pédiatrie Hôpital d`instruction Militaire, Rabat, Morocco.
R. Abikassem
Service de Pédiatrie Hôpital d`instruction Militaire, Rabat, Morocco.
*Author to whom correspondence should be addressed.
Abstract
We report 03 cases of portal cavernoma hospitalized in pediatric department. Through these observations, we will try to describe the different clinical and biological aspects and discuss the diagnostic and therapeutic approaches through a literature review. Somatic examination revealed a distended abdomen and hepatosplenomegaly, presence of collateral venous circulation. The diagnostic approach to portal cavernoma in children is based on careful clinical examination, including identification of symptoms such as gastrointestinal bleeding, hepatomegaly and signs of liver disease. The biological work-up showed bicytopenia (microcytic hypochromic anaemia with thrombocytopenia) with a normal blood and liver count. The long-term course of portal cavernoma in children depends on various factors, such as the presence of complications, response to treatment and medical and surgical management. The prognosis is generally better in children who receive regular medical follow-up and appropriate treatment in the event of complications.
Keywords: Portal cavernoma, abdominal trauma, hepatosplenomegaly, bicytopenia